OUR EXPERIENCE IN TREATMENT OF HIRSCHSPRUNG'S DISEASE IN A 18-YEAR-OLD PATIENT. CLINICAL CASE
https://doi.org/10.38181/2223-2427-2020-4-47-52
Abstract
Introduction: Hirschsprung's disease (HD) is a relatively rare condition, in which the intermuscular (Auerbach) and submucosal (Meissner) plexus are absent in the colon wall at various lengths. In the literature, HD is described mainly in relation to the pediatric surgery area of interests because up to 90% of cases of this disease are detected before the age of 5 years 6. However, in some patients, the symptoms of the disease are not severe, so patients survive to adulthood without an established diagnosis.
Clinical case: we demonstrate our experience of surgical treatment of Hirschsprung's disease in a 18-year-old patient.
Conclusion: Although Hirschsprung's disease is in most cases a disease of childhood, it is necessary to keep in mind its typical symptoms when an adult patient complains of constipation. Proper diagnosis and correctly selected surgical treatment can not only eliminate symptoms and improve quality of life, but also reduce the likelihood of serious complications.
About the Authors
M. A. Agapov
Federal State Budget Educational Institution of Higher Education M.V. Lomonosov Moscow State University (Lomonosov MSU)
Russian Federation
Russian Federation
Mikhail A. Agapov – PhD, Professor of the Department of Surgery
Leninskie Gory St., 1, 119991, Moscow
D. R. Markaryan
Federal State Budget Educational Institution of Higher Education M.V. Lomonosov Moscow State University (Lomonosov MSU)
Russian Federation
Russian Federation
Daniil R. Markaryan – PhD, docent of the Department of Surgery
Leninskie Gory St., 1, 119991, Moscow
V. V. Kakotkin
Federal State Budget Educational Institution of Higher Education M.V. Lomonosov Moscow State University (Lomonosov MSU)
Russian Federation
Russian Federation
Viktor V. Kakotkin – Department of Surgery №1 of the Medical Research Educational Center
Leninskie Gory St., 1, 119991, Moscow
A. M. Lukyanov
Federal State Autonomous Educational Institution of Higher Education I.M. Sechenov First Moscow State Medical University (Sechenov University)
Russian Federation
Russian Federation
Aleхander M. Lukyanov – 6th year student of the Filatov Clinical Institute of Children's Health
Bolshaya Pirogovskaya St., 2/4, 119435, Moscow
V. A. Kubyshkin
Federal State Budget Educational Institution of Higher Education M.V. Lomonosov Moscow State University (Lomonosov MSU)
Russian Federation
Russian Federation
Valery A. Kubyshkin – PhD, academician of RSA, Head of the Surgery department
Leninskie Gory St., 1, 119991, Moscow
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Review
For citations:
Agapov M.A., Markaryan D.R., Kakotkin V.V., Lukyanov A.M., Kubyshkin V.A. OUR EXPERIENCE IN TREATMENT OF HIRSCHSPRUNG'S DISEASE IN A 18-YEAR-OLD PATIENT. CLINICAL CASE. Surgical practice (Russia). 2021;(1):47-52. (In Russ.) https://doi.org/10.38181/2223-2427-2020-4-47-52
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